DRSC/TRiP Functional Genomics Resources

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Protein Alignment NPHS1 and nrm

DIOPT Version :10

Sequence 1:NP_004637.1 Gene:NPHS1 / 4868 HGNCID:7908 Length:1241 Species:Homo sapiens
Sequence 2:NP_001246890.1 Gene:nrm / 40515 FlyBaseID:FBgn0262509 Length:2192 Species:Drosophila melanogaster


Alignment Length:894 Identity:195/894 - (21%)
Similarity:339/894 - (37%) Gaps:181/894 - (20%)


- Green bases have known domain annotations that are detailed below.


Human    34 FWALPENLTVVEGASVELRCGVSTPGSAV-------QWAKDGLLLG------------------P 73
            |:...|......|..:|||  |..|.:.|       ...|:|.::|                  |
  Fly   132 FFIPEETCDNFNGYRIELR--VLVPPTEVVILDAKGDRIKNGSVVGPMQERQSLKATCTVRNTRP 194

Human    74 DPRIPGF------PRYRLEGDPARG------EFHLHIEACDLSDDAEYECQVGRSEMGPELVSPR 126
            .|.:..|      ..|....|...|      |....:...||:.|  .||:| :|.....:...:
  Fly   195 QPEVSWFRGTKRLTTYSPTHDLVDGLYTSTLELDWTLSREDLAQD--IECRV-KSAAIQNVTVTK 256

Human   127 VILSILVPPKLLLLTPEAGTMVTWVAGQEYVVNCVSGDAKPAPDI------TILLSGQT-ISDIS 184
            ..:.:.|.|..:.:.   |.....|.|.:.|:.|....|:||.::      ||:.||:. |:::.
  Fly   257 FSVDLQVRPTSIDIN---GVKHHTVQGSKVVLTCDIHGARPAVNLTWYNTTTIISSGENEITEVR 318

Human   185 ANVNEGSQQKLFTVEATARVTPRSSDNRQLLVCEASSPAL----EAPIKASFTVNVLFPP----G 241
            :...|.| ...|..::.........:|.::..|||.:..|    |.||.::.|:.||:||    .
  Fly   319 SKSLEKS-DGTFHTQSELIFNATRFENDRVFRCEAENIVLQINREKPISSALTLEVLYPPVVKVS 382

Human   242 PPVIEWPGLDEGHVRAGQSLELPCVARGGNP--LATLQWLKNGQPVSTAWGTEHTQAVARSV--L 302
            |..|.        ....:.:.|.| ....||  |..::|.:|...|:....|.:....:.:|  :
  Fly   383 PSAIT--------ANTSEIVLLNC-EYFANPASLTQVEWYRNDILVNVNDTTHYKGGNSENVALV 438

Human   303 VMTVRPEDHGAQLSCEAHNSVSAGTQEHGITLQVTFPPSAIIIL---GSASQTENKNVTLSCVSK 364
            :.:...||.| ..||:..|::..||.:..|.|.|.:.|:..|::   |...:::..||||.|...
  Fly   439 IKSTEKEDIG-NYSCQLSNNIGKGTSDQKINLDVQYAPTVEILMIPEGPVKESDESNVTLFCNVL 502

Human   365 SSRPRVL--LRWWLG---WRQLLPMEETVMDGLHGGHISMSNLTFLARREDNGLTLTCEAFSEA- 423
            .:.|.||  :||:..   .::|...|||..|..   ||..|.|...:.........:||.|:.| 
  Fly   503 DANPSVLTKVRWYANSTLLKELPDCEETREDLC---HIDPSKLLLESIGRGFFYNYSCEGFNAAG 564

Human   424 FTKETFKKSLILNVKYPAQKLWIEGPPEGQKLRAGTRVRLVC-LAIGGNPEPS-LMWYKDSRTVT 486
            :...:..|.|:::.: |........|....|.::   |...| :...|.||.: ..|.:..|...
  Fly   565 WGPRSEDKELLVHYE-PGPAALSHFPLVAVKKKS---VTFSCSVDDPGFPESNRFRWLRGGRGPL 625

Human   487 ESRLPQESRRVHLGSVEKSGSTFSRELVLVTGPSDNQAKFTCKA----GQ-LSASTQLAVQFPPT 546
            :..:.::      .:||..|             .|::..::|.|    |: :.|:..|.|..||.
  Fly   626 QDIVTKD------WTVEPVG-------------LDSRTNYSCYAYNEGGKGVMATVNLEVHAPPF 671

Human   547 NVTIL-ANASALRPGDALNLTCVSVSSNPPVNLSWDKEGERLEG-----------VAAPPRRAPF 599
            .:..| .....|.......||| .:...|..::||.|:|..:|.           :.|.|....|
  Fly   672 FIKNLPPYTGILHSSPNATLTC-RIECVPRCDISWQKDGVPIERNDSRYFIKEKYMDASPATGDF 735

Human   600 KGSAAARSVL-------------LQVSSRDHGQRVTCRAHSAELRETVSSFYRLNVLYRPE--FL 649
            :   :..|||             ::..:.::    :|.:....:..::.|.....:.|.||  .:
  Fly   736 E---SMLSVLHFNMPNWPDSKFNIEADNANY----SCVSTGNIVGGSIRSRTYFGIEYAPENTTV 793

Human   650 GEQVLVVTAVEQGEALLPVSV----SANPAPEAFNWTFRGYRLSPAGGPRHRILSSGALHLWN-- 708
            .|.::.|.     |..:|..|    .|||.| ::.|.|           ::..:::|...:.|  
  Fly   794 SENIVYVQ-----EDTIPGRVICKSRANPEP-SYKWIF-----------KNETIANGNALIINTA 841

Human   709 VTRADDGLYQLHCQNSEGTAEARLRLDVHYAPTIRALQDPTEVNVGGSVDIVCTVDANPILPGMF 773
            :.|.|||.|.....|..|::.|:..:.|.:.|  |...:..|::  ....::||...||| ...|
  Fly   842 MNRNDDGTYTCLAYNKHGSSIAKTVIKVQFKP--RCEIERQEID--DQDTLICTAYGNPI-EADF 901

Human   774 NWERLGEDEEDQSLDDMEKISRGPTGRLRIHHAKLAQAGAYQCIVDNGV 822
            :|....|:|.|::|...:| .........|.....|.:..|:|:.:|.|
  Fly   902 SWSIKTENETDENLGSGKK-ENSVEKSFYILQTDYAISRTYRCVANNTV 949

Known Domains:


Indicated by green bases in alignment.

GeneSequenceDomainRegion External IDIdentity
NPHS1NP_004637.1 V-set 38..119 CDD:462230 25/117 (21%)
C2-set_2 141..228 CDD:400489 22/97 (23%)
Ig strand B 156..160 CDD:409353 1/3 (33%)
Ig strand C 170..174 CDD:409353 1/9 (11%)
Ig strand E 200..204 CDD:409353 0/3 (0%)
Ig strand F 214..219 CDD:409353 1/4 (25%)
Ig strand G 229..232 CDD:409353 0/2 (0%)
Ig 237..336 CDD:472250 25/106 (24%)
Ig strand B 261..265 CDD:409353 1/3 (33%)
Ig strand C 275..279 CDD:409353 0/3 (0%)
Ig strand E 300..304 CDD:409353 1/5 (20%)
Ig strand F 314..319 CDD:409353 2/4 (50%)
Ig strand G 332..335 CDD:409353 1/2 (50%)
Ig 345..424 CDD:472250 24/87 (28%)
Ig strand B 357..361 CDD:409353 3/3 (100%)
Ig strand C 371..375 CDD:409353 2/5 (40%)
Ig strand E 400..404 CDD:409353 2/3 (67%)
Ig strand F 414..419 CDD:409353 1/4 (25%)
Ig strand G 430..433 CDD:409353 1/2 (50%)
Ig 446..541 CDD:472250 18/101 (18%)
Ig strand B 461..465 CDD:409353 1/3 (33%)
Ig strand C 475..479 CDD:409353 0/4 (0%)
Ig strand E 510..515 CDD:409353 0/4 (0%)
Ig strand F 525..530 CDD:409353 1/4 (25%)
Ig 549..632 CDD:472250 18/107 (17%)
Ig strand B 563..567 CDD:409353 1/3 (33%)
Ig strand C 577..581 CDD:409353 1/3 (33%)
Ig strand E 606..610 CDD:409353 3/16 (19%)
Ig strand F 620..625 CDD:409353 1/4 (25%)
Ig strand G 635..638 CDD:409353 1/2 (50%)
Ig 646..736 CDD:472250 23/97 (24%)
Ig strand B 664..668 CDD:409353 0/3 (0%)
Ig strand C 678..682 CDD:409353 0/3 (0%)
Ig strand E 702..706 CDD:409353 1/3 (33%)
Ig strand F 716..721 CDD:409353 1/4 (25%)
Ig strand G 729..732 CDD:409353 1/2 (50%)
Ig_3 740..820 CDD:464046 19/79 (24%)
IgC1_hNephrin_like 834..942 CDD:143250
putative Ig strand A 839..844 CDD:143250
putative Ig strand B 859..866 CDD:143250
putative Ig strand C 870..876 CDD:143250
putative Ig strand C' 879..881 CDD:143250
putative Ig strand D 888..891 CDD:143250
putative Ig strand E 898..906 CDD:143250
putative Ig strand F 917..924 CDD:143250
putative Ig strand G 939..942 CDD:143250
FN3 941..1022 CDD:238020
Disordered. /evidence=ECO:0000256|SAM:MobiDB-lite 1025..1057
Disordered. /evidence=ECO:0000256|SAM:MobiDB-lite 1099..1137
Binds to NPHS2 1160..1241
nrmNP_001246890.1 V-set 44..152 CDD:462230 6/21 (29%)
Ig strand B 183..187 CDD:409353 0/3 (0%)
Ig <185..248 CDD:472250 14/65 (22%)
Ig strand C 197..201 CDD:409353 0/3 (0%)
Ig strand E 225..229 CDD:409353 1/3 (33%)
Ig strand F 239..244 CDD:409353 3/6 (50%)
Ig strand G 253..256 CDD:409353 0/2 (0%)
Ig 277..354 CDD:472250 19/77 (25%)
Ig strand B 283..287 CDD:409353 1/3 (33%)
Ig strand C 297..301 CDD:409353 0/3 (0%)
Ig strand E 333..337 CDD:409353 0/3 (0%)
Ig strand F 347..352 CDD:409353 1/4 (25%)
Ig_3 376..456 CDD:464046 19/89 (21%)
Ig 676..779 CDD:472250 18/110 (16%)
Ig strand B 689..693 CDD:409353 1/3 (33%)
Ig strand C 702..706 CDD:409353 1/3 (33%)
Ig strand E 734..741 CDD:409353 1/9 (11%)
Ig strand F 762..767 CDD:409353 1/8 (13%)
Ig <811..869 CDD:472250 16/69 (23%)
Ig strand C 820..824 CDD:143205 0/3 (0%)
Ig strand F 849..854 CDD:143205 1/4 (25%)
Ig strand G 862..865 CDD:143205 1/2 (50%)
PTZ00112 1747..>1940 CDD:240274
Blue background indicates that the domain is not in the aligned region.

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